ЭТИОЛОГИЯ И ПАТОФИЗИОЛОГИЯ ХРОНИЧЕСКОГО ИНТЕСТИНАЛЬНОГО ПСЕВДООБСТРУКТИВНОГО СИНДРОМА У ДЕТЕЙ II часть. Первичные и вторичные хронические псевдообструктивные синдромы у детей и взрослых

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Аннотация

Хронический интестинальный псевдообструктивный синдром - редкий синдром, проявляющийся рецидивирующими явлениями кишечной непроходимости, возникающими на фоне нейропатий, миопатий или нейромиопатий врожденного или приобретенного генеза. В статье рассмотрены особенности этиопатогенеза различных форм заболевания, в том числе собраны открытые за последние десятилетия мутации de nova. Статья представляет интерес как для хирургов, которым необходимо уметь своевременно диагностировать интестинальную псевдообструкцию во избежание необоснованных операций, так и для врачей других специальностей, которые могут встретиться с данным синдромом в своей практике.

Об авторах

Юлия Валентиновна Аверьянова
Российская детская клиническая больница Минздрава России
Россия


Александр Юрьевич Разумовский
РНИМУ им. Н.И. Пирогова
Россия


Алексей Эдуардович Степанов
Российская детская клиническая больница Минздрава России
Россия


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Дополнительные файлы

Для цитирования: Аверьянова Ю.В., Разумовский А.Ю., Степанов А.Э. ЭТИОЛОГИЯ И ПАТОФИЗИОЛОГИЯ ХРОНИЧЕСКОГО ИНТЕСТИНАЛЬНОГО ПСЕВДООБСТРУКТИВНОГО СИНДРОМА У ДЕТЕЙ II часть. Первичные и вторичные хронические псевдообструктивные синдромы у детей и взрослых. Российский вестник детской хирургии, анестезиологии и реаниматологии. 2016;6(2):102-111.

For citation: Averyanova Y.V., Razumovsky A.Y., Stepanov A.E. ETIOLOGY AND PATHOPHYSIOLOGY OF CHRONIC INTESTINAL SYNDROME OF PSEUDO-OBSTRUCTION IN CHILDREN Part II. Primary and secondary chronic syndrome of pseudo-obstruction in children and adults. Russian Journal of Pediatric Surgery, Anesthesia and Intensive Care. 2016;6(2):102-111. (In Russ.)

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