ETIOLOGY AND PATHOPHYSIOLOGY OF CHRONIC INTESTINAL SYNDROME OF PSEUDO-OBSTRUCTION IN CHILDREN Part II. Primary and secondary chronic syndrome of pseudo-obstruction in children and adults

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Abstract

Chronic intestinal syndrome of pseudo-obstruction is a rare syndrome manifested through recur-rent phenomena of bowel obstruction developed against neuropathies, myopathies and neuromyo-pathies of congenital or acquired genesis. The article deals with the peculiarities of ethiopathogen-esis of different forms of the disease including de nova mutations revealed within the last decades. The article is interesting both for surgeons who must diagnose intestinal pseudo-obstruction in a timely manner to avoid unnecessary surgeries and for other doctors who can come across the syndrome during their practice.

About the authors

Yu. V. Averyanova

Russian Pediatric Clinical Hospital of the Ministry of Health of the Russian Federation

Author for correspondence.
Email: noemail@neicon.ru
Russian Federation

A. Yu. Razumovsky

State Budgetary Educational Institution of Higher Professional Education Russian National Research Medical University named after N.I. Pirogov of the Ministry of Health of the RF

Email: 1595105@mail.ru
Russian Federation

A. E. Stepanov

Russian Pediatric Clinical Hospital of the Ministry of Health of the Russian Federation

Email: operacia@rdkb.ru
Russian Federation

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