ANESTHETIC IMPLICATIONS FOR SURGICAL CORRECTION OF KYPHOSIS IN A CHILD WITH TYPE I MUCOPOLYSACCHARIDOSIS (HURLER SYNDROME): A CLINICAL CASE AND LITERATURE ANALYSIS

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Abstract

A clinical case of anesthetic management of a child with a complex and rare genetic disease such as type I mucopolysaccharidosis (Hurler syndrome) undergoing spine surgery is described. The surgery was indicated due to the presence of rapidly progressive severe deformity of the thoracolumbar section of the spine with augmentation of neurological symptoms. Risk factors are determined; the protocol and peculiarities of anesthetic management are described.

About the authors

A. N. Tretyakova

The Federal State Budgetary Institution Russian Ilizarov Scientific Center for Restorative Traumatology and Orthopaedics

Author for correspondence.
Email: anestezianik@mail.ru
Russian Federation

S. O. Ryabykh

The Federal State Budgetary Institution Russian Ilizarov Scientific Center for Restorative Traumatology and Orthopaedics

Email: rso_@mail.ru
Russian Federation

P. V. Ochirova

The Federal State Budgetary Institution Russian Ilizarov Scientific Center for Restorative Traumatology and Orthopaedics

Email: poleen@yandex.ru
Russian Federation

T. V. Ryabykh

The Federal State Budgetary Institution Russian Ilizarov Scientific Center for Restorative Traumatology and Orthopaedics

Email: rtatav@rambler.ru
Russian Federation

V. L. Shusharina

The Federal State Budgetary Institution Russian Ilizarov Scientific Center for Restorative Traumatology and Orthopaedics

Email: shusharina.vera2014@yandex.ru
Russian Federation

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Copyright (c) 2015 Tretyakova A.N., Ryabykh S.O., Ochirova P.V., Ryabykh T.V., Shusharina V.L.

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